ICD-10-CM A50: Congenital syphilis

ICD-10-CM Diagnosis Code (2025)

Official Description for A50

Congenital syphilis

Coding Notes & Guidelines for A50

Excludes1: Not Coded Here

Hutchinson's triad (A50.53)

Excludes1: Not Coded Here

Hutchinson's triad (A50.53)

Use Additional Code

code to identify any associated mental disorder

Inclusion Terms

Any congenital syphilitic condition specified as early or manifest less than two years after birth.

Inclusion Terms

Early congenital syphilitic laryngitis

Inclusion Terms

Congenital syphilis without clinical manifestations, with positive serological reaction and negative spinal fluid test, less than two years after birth.

Inclusion Terms

Congenital syphilis NOS less than two years after birth.

Inclusion Terms

Juvenile neurosyphilis NOS

Inclusion Terms
  • Dementia paralytica juvenilis
  • Juvenile taboparetic neurosyphilis
Inclusion Terms

Juvenile tabes dorsalis

Inclusion Terms

Any congenital syphilitic condition specified as late or manifest two years or more after birth.

Inclusion Terms

Congenital syphilis without clinical manifestations, with positive serological reaction and negative spinal fluid test, two years or more after birth.

Inclusion Terms

Congenital syphilis NOS two years or more after birth.

Child Codes (More Specific Codes for A50):

A50.0 - Early congenital syphilis, symptomatic A50.01 - Early congenital syphilitic oculopathy A50.02 - Early congenital syphilitic osteochondropathy A50.03 - Early congenital syphilitic pharyngitis A50.04 - Early congenital syphilitic pneumonia A50.05 - Early congenital syphilitic rhinitis A50.06 - Early cutaneous congenital syphilis A50.07 - Early mucocutaneous congenital syphilis A50.08 - Early visceral congenital syphilis A50.09 - Other early congenital syphilis, symptomatic A50.1 - Early congenital syphilis, latent A50.2 - Early congenital syphilis, unspecified A50.3 - Late congenital syphilitic oculopathy A50.30 - Late congenital syphilitic oculopathy, unspecified A50.31 - Late congenital syphilitic interstitial keratitis A50.32 - Late congenital syphilitic chorioretinitis A50.39 - Other late congenital syphilitic oculopathy A50.4 - Late congenital neurosyphilis [juvenile neurosyphilis] A50.40 - Late congenital neurosyphilis, unspecified A50.41 - Late congenital syphilitic meningitis A50.42 - Late congenital syphilitic encephalitis A50.43 - Late congenital syphilitic polyneuropathy A50.44 - Late congenital syphilitic optic nerve atrophy A50.45 - Juvenile general paresis A50.49 - Other late congenital neurosyphilis A50.5 - Other late congenital syphilis, symptomatic A50.51 - Clutton's joints A50.52 - Hutchinson's teeth A50.53 - Hutchinson's triad A50.54 - Late congenital cardiovascular syphilis A50.55 - Late congenital syphilitic arthropathy A50.56 - Late congenital syphilitic osteochondropathy A50.57 - Syphilitic saddle nose A50.59 - Other late congenital syphilis, symptomatic A50.6 - Late congenital syphilis, latent A50.7 - Late congenital syphilis, unspecified A50.9 - Congenital syphilis, unspecified

About ICD-10-CM Code A50 (Congenital syphilis)

ICD-10-CM code A50 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM A50 became effective on October 1, 2024.

This page provides detailed information about A50 - Congenital syphilis. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Congenital syphilis.