ICD-10-CM C00: Malignant neoplasm of lip

ICD-10-CM Diagnosis Code (2025)

Official Description for C00

Malignant neoplasm of lip

Coding Notes & Guidelines for C00

Excludes1: Not Coded Here
  • malignant melanoma of lip (C43.0)
  • Merkel cell carcinoma of lip (C4A.0)
  • other and unspecified malignant neoplasm of skin of lip (C44.0-)
Use Additional Code
  • code to identify:
  • alcohol abuse and dependence (F10.-)
  • history of tobacco dependence (Z87.891)
  • tobacco dependence (F17.-)
  • tobacco use (Z72.0)
Inclusion Terms
  • Malignant neoplasm of lipstick area of upper lip
  • Malignant neoplasm of upper lip NOS
  • Malignant neoplasm of vermilion border of upper lip
Inclusion Terms
  • Malignant neoplasm of lower lip NOS
  • Malignant neoplasm of lipstick area of lower lip
  • Malignant neoplasm of vermilion border of lower lip
Inclusion Terms

Malignant neoplasm of vermilion border of lip NOS

Inclusion Terms
  • Malignant neoplasm of buccal aspect of upper lip
  • Malignant neoplasm of frenulum of upper lip
  • Malignant neoplasm of mucosa of upper lip
  • Malignant neoplasm of oral aspect of upper lip
Inclusion Terms
  • Malignant neoplasm of buccal aspect of lower lip
  • Malignant neoplasm of frenulum of lower lip
  • Malignant neoplasm of mucosa of lower lip
  • Malignant neoplasm of oral aspect of lower lip
Inclusion Terms
  • Malignant neoplasm of buccal aspect of lip, unspecified
  • Malignant neoplasm of frenulum of lip, unspecified
  • Malignant neoplasm of mucosa of lip, unspecified
  • Malignant neoplasm of oral aspect of lip, unspecified

Child Codes (More Specific Codes for C00):

C00.0 - Malignant neoplasm of external upper lip C00.1 - Malignant neoplasm of external lower lip C00.2 - Malignant neoplasm of external lip, unspecified C00.3 - Malignant neoplasm of upper lip, inner aspect C00.4 - Malignant neoplasm of lower lip, inner aspect C00.5 - Malignant neoplasm of lip, unspecified, inner aspect C00.6 - Malignant neoplasm of commissure of lip, unspecified C00.8 - Malignant neoplasm of overlapping sites of lip C00.9 - Malignant neoplasm of lip, unspecified

About ICD-10-CM Code C00 (Malignant neoplasm of lip)

ICD-10-CM code C00 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM C00 became effective on October 1, 2024.

This page provides detailed information about C00 - Malignant neoplasm of lip. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Malignant neoplasm of lip.