ICD-10-CM D47: Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue

ICD-10-CM Diagnosis Code (2025)

Official Description for D47

Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue

Coding Notes & Guidelines for D47

Excludes1: Not Coded Here
  • congenital cutaneous mastocytosis (Q82.2)
  • histiocytic neoplasms of uncertain behavior (D47.Z9)
  • malignant mast cell neoplasm (C96.2-)
Excludes1: Not Coded Here
  • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
  • congenital urticaria pigmentosa (Q82.2)
  • extracutaneous mastocytoma (D47.09)
Excludes1: Not Coded Here
  • aggressive systemic mastocytosis (C96.21)
  • mast cell leukemia (C94.3-)
Excludes1: Not Coded Here
  • atypical chronic myeloid leukemia BCR/ABL-negative (C92.2-)
  • chronic myeloid leukemia BCR/ABL-positive (C92.1-)
  • myelofibrosis NOS (D75.81)
  • myelophthisic anemia (D61.82)
  • myelophthisis (D61.82)
  • secondary myelofibrosis NOS (D75.81)
Excludes1: Not Coded Here

acute myelofibrosis (C94.4-)

Excludes2: Not Included Here
  • reactive thrombocytosis (D75.838)
  • secondary thrombocytosis (D75.838)
  • thrombocythemia NOS (D75.839)
  • thrombocytosis NOS (D75.839)
Excludes2: Not Included Here

Kaposi's sarcoma (C46.-)

Code First

complications of transplanted organs and tissue (T86.-)

Inclusion Terms
  • Diffuse cutaneous mastocytosis
  • Maculopapular cutaneous mastocytosis
  • Solitary mastocytoma
  • Telangiectasia macularis eruptiva perstans
  • Urticaria pigmentosa
Inclusion Terms
  • Indolent systemic mastocytosis
  • Isolated bone marrow mastocytosis
  • Smoldering systemic mastocytosis
  • Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Inclusion Terms
  • Extracutaneous mastocytoma
  • Mast cell tumor NOS
  • Mastocytoma NOS
  • Mastocytosis NOS
Inclusion Terms
  • Chronic neutrophilic leukemia
  • Myeloproliferative disease, unspecified
Inclusion Terms

Monoclonal gammopathy of undetermined significance [MGUS]

Inclusion Terms
  • Essential thrombocytosis
  • Idiopathic hemorrhagic thrombocythemia
  • Primary thrombocytosis
Inclusion Terms
  • Chronic idiopathic myelofibrosis
  • Myelofibrosis (idiopathic) (with myeloid metaplasia)
  • Myelosclerosis (megakaryocytic) with myeloid metaplasia
  • Secondary myelofibrosis in myeloproliferative disease
Inclusion Terms

Histiocytic tumors of uncertain behavior

Inclusion Terms

Lymphoproliferative disease NOS

Code Also
  • , if applicable, any associated hematological non-mast cell lineage disease, such as:
  • acute myeloid leukemia (C92.6-, C92.A-)
  • chronic myelomonocytic leukemia (C93.1-)
  • essential thrombocytosis (D47.3)
  • hypereosinophilic syndrome (D72.1)
  • myelodysplastic syndrome (D46.9)
  • myeloproliferative syndrome (D47.1)
  • non-Hodgkin lymphoma (C82-C85)
  • plasma cell myeloma (C90.0-)
  • polycythemia vera (D45)
Code Also

, if applicable, human herpesvirus 8 infection (B10.89)

Child Codes (More Specific Codes for D47):

D47.0 - Mast cell neoplasms of uncertain behavior D47.01 - Cutaneous mastocytosis D47.02 - Systemic mastocytosis D47.09 - Other mast cell neoplasms of uncertain behavior D47.1 - Chronic myeloproliferative disease D47.2 - Monoclonal gammopathy D47.3 - Essential (hemorrhagic) thrombocythemia D47.4 - Osteomyelofibrosis D47.9 - Neoplasm of uncertain behavior of lymphoid, hematopoietic and related tissue, unspecified D47.Z - Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue D47.Z1 - Post-transplant lymphoproliferative disorder (PTLD) D47.Z2 - Castleman disease D47.Z9 - Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue

About ICD-10-CM Code D47 (Other neoplasms of uncertain behavior of lymphoid)

ICD-10-CM code D47 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM D47 became effective on October 1, 2024.

This page provides detailed information about D47 - Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Other neoplasms of uncertain behavior of lymphoid related to hematopoietic and related tissue.