ICD-10-CM D47.0: Mast cell neoplasms of uncertain behavior

ICD-10-CM Diagnosis Code (2025)

Official Description for D47.0

Mast cell neoplasms of uncertain behavior

Coding Notes & Guidelines for D47.0

Excludes1: Not Coded Here
  • congenital cutaneous mastocytosis (Q82.2)
  • histiocytic neoplasms of uncertain behavior (D47.Z9)
  • malignant mast cell neoplasm (C96.2-)
Excludes1: Not Coded Here
  • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
  • congenital urticaria pigmentosa (Q82.2)
  • extracutaneous mastocytoma (D47.09)
Excludes1: Not Coded Here
  • aggressive systemic mastocytosis (C96.21)
  • mast cell leukemia (C94.3-)
Inclusion Terms
  • Diffuse cutaneous mastocytosis
  • Maculopapular cutaneous mastocytosis
  • Solitary mastocytoma
  • Telangiectasia macularis eruptiva perstans
  • Urticaria pigmentosa
Inclusion Terms
  • Indolent systemic mastocytosis
  • Isolated bone marrow mastocytosis
  • Smoldering systemic mastocytosis
  • Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Inclusion Terms
  • Extracutaneous mastocytoma
  • Mast cell tumor NOS
  • Mastocytoma NOS
  • Mastocytosis NOS
Code Also
  • , if applicable, any associated hematological non-mast cell lineage disease, such as:
  • acute myeloid leukemia (C92.6-, C92.A-)
  • chronic myelomonocytic leukemia (C93.1-)
  • essential thrombocytosis (D47.3)
  • hypereosinophilic syndrome (D72.1)
  • myelodysplastic syndrome (D46.9)
  • myeloproliferative syndrome (D47.1)
  • non-Hodgkin lymphoma (C82-C85)
  • plasma cell myeloma (C90.0-)
  • polycythemia vera (D45)

Parent Code (Less Specific):

D47 - Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue

About ICD-10-CM Code D47.0 (Mast cell neoplasms of uncertain behavior)

ICD-10-CM code D47.0 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM D47.0 became effective on October 1, 2024.

This page provides detailed information about D47.0 - Mast cell neoplasms of uncertain behavior. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Mast cell neoplasms of uncertain behavior.