ICD-10-CM D55: Anemia due to enzyme disorders

ICD-10-CM Diagnosis Code (2025)

Official Description for D55

Anemia due to enzyme disorders

Coding Notes & Guidelines for D55

Excludes1: Not Coded Here

drug-induced enzyme deficiency anemia (D59.2)

Excludes1: Not Coded Here

glucose-6-phosphate dehydrogenase (G6PD) deficiency without anemia (D75.A)

Excludes1: Not Coded Here

disorders of glycolysis not associated with anemia (E74.81-)

Inclusion Terms
  • Favism
  • G6PD deficiency anemia
Inclusion Terms
  • Anemia (due to) enzyme deficiencies, except G6PD, related to the hexose monophosphate [HMP] shunt pathway
  • Anemia (due to) hemolytic nonspherocytic (hereditary), type I
Inclusion Terms
  • PK deficiency anemia
  • Pyruvate kinase deficiency anemia
Inclusion Terms
  • Hexokinase deficiency anemia
  • Triose-phosphate isomerase deficiency anemia

Child Codes (More Specific Codes for D55):

About ICD-10-CM Code D55 (Anemia due to enzyme disorders)

ICD-10-CM code D55 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM D55 became effective on October 1, 2024.

This page provides detailed information about D55 - Anemia due to enzyme disorders. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Anemia due to enzyme disorders.