ICD-10-CM D56: Thalassemia

ICD-10-CM Diagnosis Code (2025)

Official Description for D56

Thalassemia

Coding Notes & Guidelines for D56

Excludes1: Not Coded Here

sickle-cell thalassemia (D57.4-)

Excludes1: Not Coded Here
  • alpha thalassemia trait or minor (D56.3)
  • asymptomatic alpha thalassemia (D56.3)
  • hydrops fetalis due to isoimmunization (P56.0)
  • hydrops fetalis not due to immune hemolysis (P83.2)
Excludes1: Not Coded Here
  • beta thalassemia minor (D56.3)
  • beta thalassemia trait (D56.3)
  • delta-beta thalassemia (D56.2)
  • hemoglobin E-beta thalassemia (D56.5)
  • sickle-cell beta thalassemia (D57.4-)
Excludes1: Not Coded Here
  • delta-beta thalassemia minor (D56.3)
  • delta-beta thalassemia trait (D56.3)
Excludes1: Not Coded Here
  • alpha thalassemia (D56.0)
  • beta thalassemia (D56.1)
  • delta-beta thalassemia (D56.2)
  • hemoglobin E-beta thalassemia (D56.5)
  • sickle-cell trait (D57.3)
Excludes1: Not Coded Here
  • beta thalassemia (D56.1)
  • beta thalassemia minor (D56.3)
  • beta thalassemia trait (D56.3)
  • delta-beta thalassemia (D56.2)
  • delta-beta thalassemia trait (D56.3)
  • hemoglobin E disease (D58.2)
  • other hemoglobinopathies (D58.2)
  • sickle-cell beta thalassemia (D57.4-)
Excludes1: Not Coded Here
  • hemoglobin C disease (D58.2)
  • hemoglobin E disease (D58.2)
  • other hemoglobinopathies (D58.2)
  • sickle-cell anemia (D57.-)
  • sickle-cell thalassemia (D57.4-)
Use Additional Code

code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99)

Inclusion Terms
  • Alpha thalassemia major
  • Hemoglobin H Constant Spring
  • Hemoglobin H disease
  • Hydrops fetalis due to alpha thalassemia
  • Severe alpha thalassemia
  • Triple gene defect alpha thalassemia
Inclusion Terms
  • Beta thalassemia major
  • Cooley's anemia
  • Homozygous beta thalassemia
  • Severe beta thalassemia
  • Thalassemia intermedia
  • Thalassemia major
Inclusion Terms

Homozygous delta-beta thalassemia

Inclusion Terms
  • Alpha thalassemia minor
  • Alpha thalassemia silent carrier
  • Alpha thalassemia trait
  • Beta thalassemia minor
  • Beta thalassemia trait
  • Delta-beta thalassemia minor
  • Delta-beta thalassemia trait
  • Thalassemia trait NOS
Inclusion Terms
  • Dominant thalassemia
  • Hemoglobin C thalassemia
  • Mixed thalassemia
  • Thalassemia with other hemoglobinopathy
Inclusion Terms

Mediterranean anemia (with other hemoglobinopathy)

Child Codes (More Specific Codes for D56):

About ICD-10-CM Code D56 (Thalassemia)

ICD-10-CM code D56 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM D56 became effective on October 1, 2024.

This page provides detailed information about D56 - Thalassemia. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Thalassemia.