ICD-10-CM D57: Sickle-cell disorders

ICD-10-CM Diagnosis Code (2025)

Official Description for D57

Sickle-cell disorders

Coding Notes & Guidelines for D57

Excludes1: Not Coded Here

other hemoglobinopathies (D58.-)

Use Additional Code

code for any associated fever (R50.81)

Use Additional Code
  • code to identify complications, such as:
  • cholelithiasis (K80.-)
  • priapism (N48.32)
Use Additional Code
  • code to identify complications, such as:
  • cholelithiasis (K80.-)
  • priapism (N48.32)
Use Additional Code
  • code to identify complications, such as:
  • cholelithiasis (K80.-)
  • priapism (N48.32)
Use Additional Code
  • code to identify complications, such as:
  • cholelithiasis (K80.-)
  • priapism (N48.32)
Use Additional Code
  • code to identify complications, such as:
  • cholelithiasis (K80.-)
  • priapism (N48.32)
Use Additional Code
  • code to identify complications, such as:
  • cholelithiasis (K80.-)
  • priapism (N48.32)
Inclusion Terms
  • Sickle-cell disease with crisis
  • Hb-SS disease with (vaso-occlusive) pain
Inclusion Terms
  • Hb-SS disease with (painful) crisis NOS
  • Hb-SS disease with (vaso-occlusive) pain NOS
Inclusion Terms
  • Hb-SS disease without crisis
  • Sickle-cell anemia NOS
  • Sickle-cell disease NOS
  • Sickle-cell disorder NOS
Inclusion Terms
  • Hb-SC disease
  • Hb-S/Hb-C disease
Inclusion Terms
  • Sickle-cell/Hb-C disease with crisis NOS
  • Sickle-cell/Hb-C disease with (vaso-occlusive) pain NOS
Inclusion Terms
  • Hb-S trait
  • Heterozygous hemoglobin S
Inclusion Terms
  • Sickle-cell beta thalassemia
  • Thalassemia Hb-S disease
Inclusion Terms
  • Microdrepanocytosis
  • Sickle-cell thalassemia NOS
Inclusion Terms
  • Sickle-cell thalassemia with (painful) crisis NOS
  • Sickle-cell thalassemia with (vaso-occlusive) pain NOS
Inclusion Terms
  • Sickle-cell thalassemia with (painful) crisis NOS
  • Sickle-cell thalassemia with (vaso-occlusive) pain NOS
Inclusion Terms
  • HbS-beta zero without crisis
  • Sickle-cell beta zero without crisis
Inclusion Terms
  • HbS-beta zero with crisis
  • Sickle-cell beta zero with crisis
Inclusion Terms
  • HbS-beta zero with acute chest syndrome
  • Sickle-cell beta zero with acute chest syndrome
Inclusion Terms
  • HbS-beta zero with splenic sequestration
  • Sickle-cell beta zero with splenic sequestration
Inclusion Terms
  • HbS-beta zero with cerebral vascular involvement
  • Sickle-cell beta zero with cerebral vascular involvement
Inclusion Terms
  • HbS-beta zero with other specified complication
  • Sickle-cell beta zero with other specified complication
Inclusion Terms
  • HbS-beta zero with other specified complication
  • Sickle-cell beta zero with crisis unspecified
  • Sickle-cell thalassemia beta zero with (painful) crisis NOS
  • Sickle-cell thalassemia beta zero with (vaso-occlusive) pain NOS
Inclusion Terms
  • HbS-beta plus without crisis
  • Sickle-cell beta plus without crisis
Inclusion Terms
  • HbS-beta plus with crisis
  • Sickle-cell beta plus with crisis
Inclusion Terms
  • HbS-beta plus with acute chest syndrome
  • Sickle-cell beta plus with acute chest syndrome
Inclusion Terms
  • HbS-beta plus with splenic sequestration
  • Sickle-cell beta plus with splenic sequestration
Inclusion Terms
  • HbS-beta plus with cerebral vascular involvement
  • Sickle-cell beta plus with cerebral vascular involvement
Inclusion Terms
  • HbS-beta plus with crisis with other specified complication
  • Sickle-cell beta plus with crisis with other specified complication
Inclusion Terms
  • HbS-beta plus with crisis with unspecified complication
  • Sickle-cell beta plus with crisis with unspecified complication
  • Sickle-cell thalassemia beta plus with (painful) crisis NOS
  • Sickle-cell thalassemia beta plus with (vaso-occlusive) pain NOS
Inclusion Terms
  • Hb-SD disease
  • Hb-SE disease
Inclusion Terms
  • Other sickle-cell disorders with crisis NOS
  • Other sickle-cell disorders with (vaso-occlusive) pain NOS
Code Also

, if applicable, cerebral infarction (I63.-)

Code Also

, if applicable, cerebral infarction (I63.-)

Code Also

, if applicable cerebral infarction (I63.-)

Code Also

, if applicable cerebral infarction (I63.-)

Code Also

, if applicable cerebral infarction (I63.-)

Code Also

, if applicable: cerebral infarction (I63.-)

Child Codes (More Specific Codes for D57):

D57.0 - Hb-SS disease with crisis D57.00 - Hb-SS disease with crisis, unspecified D57.01 - Hb-SS disease with acute chest syndrome D57.02 - Hb-SS disease with splenic sequestration D57.03 - Hb-SS disease with cerebral vascular involvement D57.04 - Hb-SS disease with dactylitis D57.09 - Hb-SS disease with crisis with other specified complication D57.1 - Sickle-cell disease without crisis D57.2 - Sickle-cell/Hb-C disease D57.20 - Sickle-cell/Hb-C disease without crisis D57.21 - Sickle-cell/Hb-C disease with crisis D57.211 - Sickle-cell/Hb-C disease with acute chest syndrome D57.212 - Sickle-cell/Hb-C disease with splenic sequestration D57.213 - Sickle-cell/Hb-C disease with cerebral vascular involvement D57.214 - Sickle-cell/Hb-C disease with dactylitis D57.218 - Sickle-cell/Hb-C disease with crisis with other specified complication D57.219 - Sickle-cell/Hb-C disease with crisis, unspecified D57.3 - Sickle-cell trait D57.4 - Sickle-cell thalassemia D57.40 - Sickle-cell thalassemia without crisis D57.41 - Sickle-cell thalassemia, unspecified, with crisis D57.411 - Sickle-cell thalassemia, unspecified, with acute chest syndrome D57.412 - Sickle-cell thalassemia, unspecified, with splenic sequestration D57.413 - Sickle-cell thalassemia, unspecified, with cerebral vascular involvement D57.414 - Sickle-cell thalassemia, unspecified, with dactylitis D57.418 - Sickle-cell thalassemia, unspecified, with crisis with other specified complication D57.419 - Sickle-cell thalassemia, unspecified, with crisis D57.42 - Sickle-cell thalassemia beta zero without crisis D57.43 - Sickle-cell thalassemia beta zero with crisis D57.431 - Sickle-cell thalassemia beta zero with acute chest syndrome D57.432 - Sickle-cell thalassemia beta zero with splenic sequestration D57.433 - Sickle-cell thalassemia beta zero with cerebral vascular involvement D57.434 - Sickle-cell thalassemia beta zero with dactylitis D57.438 - Sickle-cell thalassemia beta zero with crisis with other specified complication D57.439 - Sickle-cell thalassemia beta zero with crisis, unspecified D57.44 - Sickle-cell thalassemia beta plus without crisis D57.45 - Sickle-cell thalassemia beta plus with crisis D57.451 - Sickle-cell thalassemia beta plus with acute chest syndrome D57.452 - Sickle-cell thalassemia beta plus with splenic sequestration D57.453 - Sickle-cell thalassemia beta plus with cerebral vascular involvement D57.454 - Sickle-cell thalassemia beta plus with dactylitis D57.458 - Sickle-cell thalassemia beta plus with crisis with other specified complication D57.459 - Sickle-cell thalassemia beta plus with crisis, unspecified D57.8 - Other sickle-cell disorders D57.80 - Other sickle-cell disorders without crisis D57.81 - Other sickle-cell disorders with crisis D57.811 - Other sickle-cell disorders with acute chest syndrome D57.812 - Other sickle-cell disorders with splenic sequestration D57.813 - Other sickle-cell disorders with cerebral vascular involvement D57.814 - Other sickle-cell disorders with dactylitis D57.818 - Other sickle-cell disorders with crisis with other specified complication D57.819 - Other sickle-cell disorders with crisis, unspecified

About ICD-10-CM Code D57 (Sickle-cell disorders)

ICD-10-CM code D57 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM D57 became effective on October 1, 2024.

This page provides detailed information about D57 - Sickle-cell disorders. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Sickle-cell disorders.