ICD-10-CM D61.0: Constitutional aplastic anemia

ICD-10-CM Diagnosis Code (2025)

Official Description for D61.0

Constitutional aplastic anemia

Coding Notes & Guidelines for D61.0

Excludes1: Not Coded Here

acquired red cell aplasia (D60.9)

Excludes1: Not Coded Here

Fanconi syndrome (E72.0-)

Use Additional Code

code, if applicable, for genetic susceptibility to other malignant neoplasm (Z15.09)

Inclusion Terms
  • Blackfan-Diamond syndrome
  • Congenital (pure) red cell aplasia
  • Familial hypoplastic anemia
  • Primary (pure) red cell aplasia
  • Red cell (pure) aplasia of infants
Inclusion Terms
  • Fanconi pancytopenia
  • Fanconi's anemia
Inclusion Terms

Pancytopenia with malformations

Code Also
  • , if applicable, associated conditions such as:
  • acute myeloblastic leukemia (C92.0-)
  • exocrine pancreatic insufficiency (K86.81)
  • myelodysplastic syndrome (D46.-)

Parent Code (Less Specific):

About ICD-10-CM Code D61.0 (Constitutional aplastic anemia)

ICD-10-CM code D61.0 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM D61.0 became effective on October 1, 2024.

This page provides detailed information about D61.0 - Constitutional aplastic anemia. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Constitutional aplastic anemia.