ICD-10-CM Diagnosis Code (2025)
Official Description for D68
Other coagulation defects
Coding Notes & Guidelines for D68
abnormal coagulation profile NOS (R79.1)
- capillary fragility (hereditary) (D69.8)
- factor VIII deficiency NOS (D66)
- factor VIII deficiency with functional defect (D66)
- antiphospholipid antibody, finding without diagnosis (R76.0)
- antiphospholipid antibody syndrome (D68.61)
- antiphospholipid antibody with hypercoagulable state (D68.61)
- lupus anticoagulant (LAC) finding without diagnosis (R76.0)
- lupus anticoagulant (LAC) with hypercoagulable state (D68.62)
- systemic lupus erythematosus [SLE] inhibitor finding without diagnosis (R76.0)
- systemic lupus erythematosus [SLE] inhibitor with hypercoagulable state (D68.62)
vitamin K deficiency of newborn (P53)
- antiphospholipid syndrome (D68.61)
- lupus anticoagulant (D68.62)
- secondary activated protein C resistance (D68.69)
- secondary antiphospholipid antibody syndrome (D68.69)
- secondary lupus anticoagulant with hypercoagulable state (D68.69)
- secondary systemic lupus erythematosus [SLE] inhibitor with hypercoagulable state (D68.69)
- systemic lupus erythematosus [SLE] inhibitor finding without diagnosis (R76.0)
- systemic lupus erythematosus [SLE] inhibitor with hemorrhagic disorder (D68.312)
- thrombotic thrombocytopenic purpura (M31.19)
- diffuse or disseminated intravascular coagulation [DIC] (D65)
- heparin induced thrombocytopenia (HIT) (D75.82-)
- hyperhomocysteinemia (E72.11)
- anti-phospholipid antibody, finding without diagnosis (R76.0)
- anti-phospholipid antibody with hemorrhagic disorder (D68.312)
- lupus anticoagulant syndrome (D68.62)
- anticardiolipin syndrome (D68.61)
- antiphospholipid syndrome (D68.61)
- lupus anticoagulant (LAC) finding without diagnosis (R76.0)
- lupus anticoagulant (LAC) with hemorrhagic disorder (D68.312)
hemorrhagic disease of newborn (P53)
- coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
- coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
code for adverse effect, if applicable, to identify drug (T45.515, T45.525)
- Partial quantitative deficiency of von Willebrand factor
- Type 1C von Willebrand disease
Qualitative defects of von Willebrand factor
Qualitative defects of von Willebrand factor with decreased platelet adhesion and selective deficiency of high-molecular-weight multimers
- Qualitative defects of von Willebrand factor with high-molecular-weight von Willebrand factor loss
- Qualitative defects of von Willebrand factor with hyper-adhesive forms
- Qualitative defects of von Willebrand factor with increased affinity for platelet glycoprotein lb
Qualitative defects of von Willebrand factor with defective platelet adhesion with a normal size distribution of von Willebrand factor multimers
- Qualitative defects of von Willebrand factor with defective von Willebrand factor to factor VIII binding
- Qualitative defects of von Willebrand factor with markedly decreased affinity for factor VIII
Qualitative defect in von Willebrand factor function, with no further subtyping
- (Near) complete absence of von Willebrand factor
- Total quantitative deficiency of von Willebrand factor
Acquired von Willebrand syndrome
- Platelet-type von Willebrand disease
- Pseudo-von Willebrand disease
- Hemophilia C
- Plasma thromboplastin antecedent [PTA] deficiency
- Rosenthal's disease
- AC globulin deficiency
- Congenital afibrinogenemia
- Deficiency of factor I [fibrinogen]
- Deficiency of factor II [prothrombin]
- Deficiency of factor V [labile]
- Deficiency of factor VII [stable]
- Deficiency of factor X [Stuart-Prower]
- Deficiency of factor XII [Hageman]
- Deficiency of factor XIII [fibrin stabilizing]
- Dysfibrinogenemia (congenital)
- Hypoproconvertinemia
- Owren's disease
- Proaccelerin deficiency
- Autoimmune hemophilia
- Autoimmune inhibitors to clotting factors
- Secondary hemophilia
- Lupus anticoagulant (LAC) with hemorrhagic disorder
- Systemic lupus erythematosus [SLE] inhibitor with hemorrhagic disorder
- Antithromboplastinemia
- Antithromboplastinogenemia
- Hemorrhagic disorder due to intrinsic increase in antithrombin
- Hemorrhagic disorder due to intrinsic increase in anti-VIIIa
- Hemorrhagic disorder due to intrinsic increase in anti-IXa
- Hemorrhagic disorder due to intrinsic increase in anti-XIa
- Drug-induced hemorrhagic disorder
- Hemorrhagic disorder due to increase in anti-IIa
- Hemorrhagic disorder due to increase in anti-Xa
- Hyperheparinemia
- Deficiency of coagulation factor due to liver disease
- Deficiency of coagulation factor due to vitamin K deficiency
Primary hypercoagulable states
Factor V Leiden mutation
- Antithrombin III deficiency
- Hypercoagulable state NOS
- Primary hypercoagulable state NEC
- Primary thrombophilia NEC
- Protein C deficiency
- Protein S deficiency
- Thrombophilia NOS
Other hypercoagulable states
- Anticardiolipin syndrome
- Antiphospholipid antibody syndrome
- Lupus anticoagulant
- Presence of systemic lupus erythematosus [SLE] inhibitor
- COVID-19 associated hypercoagulability
- Hypercoagulable states NEC
- Secondary hypercoagulable state NOS
COVID-19 associated coagulopathy
, if applicable, qualitative platelet defects (D69.1)
, if applicable, associated condition
, if applicable, associated condition
Child Codes (More Specific Codes for D68):
About ICD-10-CM Code D68 (Other coagulation defects)
ICD-10-CM code D68 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM D68 became effective on October 1, 2024.
This page provides detailed information about D68 - Other coagulation defects. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Other coagulation defects.