ICD-10-CM D68: Other coagulation defects

ICD-10-CM Diagnosis Code (2025)

Official Description for D68

Other coagulation defects

Coding Notes & Guidelines for D68

Excludes1: Not Coded Here

abnormal coagulation profile NOS (R79.1)

Excludes1: Not Coded Here
  • capillary fragility (hereditary) (D69.8)
  • factor VIII deficiency NOS (D66)
  • factor VIII deficiency with functional defect (D66)
Excludes1: Not Coded Here
  • antiphospholipid antibody, finding without diagnosis (R76.0)
  • antiphospholipid antibody syndrome (D68.61)
  • antiphospholipid antibody with hypercoagulable state (D68.61)
  • lupus anticoagulant (LAC) finding without diagnosis (R76.0)
  • lupus anticoagulant (LAC) with hypercoagulable state (D68.62)
  • systemic lupus erythematosus [SLE] inhibitor finding without diagnosis (R76.0)
  • systemic lupus erythematosus [SLE] inhibitor with hypercoagulable state (D68.62)
Excludes1: Not Coded Here

vitamin K deficiency of newborn (P53)

Excludes1: Not Coded Here
  • antiphospholipid syndrome (D68.61)
  • lupus anticoagulant (D68.62)
  • secondary activated protein C resistance (D68.69)
  • secondary antiphospholipid antibody syndrome (D68.69)
  • secondary lupus anticoagulant with hypercoagulable state (D68.69)
  • secondary systemic lupus erythematosus [SLE] inhibitor with hypercoagulable state (D68.69)
  • systemic lupus erythematosus [SLE] inhibitor finding without diagnosis (R76.0)
  • systemic lupus erythematosus [SLE] inhibitor with hemorrhagic disorder (D68.312)
  • thrombotic thrombocytopenic purpura (M31.19)
Excludes1: Not Coded Here
  • diffuse or disseminated intravascular coagulation [DIC] (D65)
  • heparin induced thrombocytopenia (HIT) (D75.82-)
  • hyperhomocysteinemia (E72.11)
Excludes1: Not Coded Here
  • anti-phospholipid antibody, finding without diagnosis (R76.0)
  • anti-phospholipid antibody with hemorrhagic disorder (D68.312)
  • lupus anticoagulant syndrome (D68.62)
Excludes1: Not Coded Here
  • anticardiolipin syndrome (D68.61)
  • antiphospholipid syndrome (D68.61)
  • lupus anticoagulant (LAC) finding without diagnosis (R76.0)
  • lupus anticoagulant (LAC) with hemorrhagic disorder (D68.312)
Excludes1: Not Coded Here

hemorrhagic disease of newborn (P53)

Excludes2: Not Included Here
  • coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
  • coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
Use Additional Code

code for adverse effect, if applicable, to identify drug (T45.515, T45.525)

Inclusion Terms
  • Partial quantitative deficiency of von Willebrand factor
  • Type 1C von Willebrand disease
Inclusion Terms

Qualitative defects of von Willebrand factor

Inclusion Terms

Qualitative defects of von Willebrand factor with decreased platelet adhesion and selective deficiency of high-molecular-weight multimers

Inclusion Terms
  • Qualitative defects of von Willebrand factor with high-molecular-weight von Willebrand factor loss
  • Qualitative defects of von Willebrand factor with hyper-adhesive forms
  • Qualitative defects of von Willebrand factor with increased affinity for platelet glycoprotein lb
Inclusion Terms

Qualitative defects of von Willebrand factor with defective platelet adhesion with a normal size distribution of von Willebrand factor multimers

Inclusion Terms
  • Qualitative defects of von Willebrand factor with defective von Willebrand factor to factor VIII binding
  • Qualitative defects of von Willebrand factor with markedly decreased affinity for factor VIII
Inclusion Terms

Qualitative defect in von Willebrand factor function, with no further subtyping

Inclusion Terms
  • (Near) complete absence of von Willebrand factor
  • Total quantitative deficiency of von Willebrand factor
Inclusion Terms

Acquired von Willebrand syndrome

Inclusion Terms
  • Platelet-type von Willebrand disease
  • Pseudo-von Willebrand disease
Inclusion Terms
  • Hemophilia C
  • Plasma thromboplastin antecedent [PTA] deficiency
  • Rosenthal's disease
Inclusion Terms
  • AC globulin deficiency
  • Congenital afibrinogenemia
  • Deficiency of factor I [fibrinogen]
  • Deficiency of factor II [prothrombin]
  • Deficiency of factor V [labile]
  • Deficiency of factor VII [stable]
  • Deficiency of factor X [Stuart-Prower]
  • Deficiency of factor XII [Hageman]
  • Deficiency of factor XIII [fibrin stabilizing]
  • Dysfibrinogenemia (congenital)
  • Hypoproconvertinemia
  • Owren's disease
  • Proaccelerin deficiency
Inclusion Terms
  • Autoimmune hemophilia
  • Autoimmune inhibitors to clotting factors
  • Secondary hemophilia
Inclusion Terms
  • Lupus anticoagulant (LAC) with hemorrhagic disorder
  • Systemic lupus erythematosus [SLE] inhibitor with hemorrhagic disorder
Inclusion Terms
  • Antithromboplastinemia
  • Antithromboplastinogenemia
  • Hemorrhagic disorder due to intrinsic increase in antithrombin
  • Hemorrhagic disorder due to intrinsic increase in anti-VIIIa
  • Hemorrhagic disorder due to intrinsic increase in anti-IXa
  • Hemorrhagic disorder due to intrinsic increase in anti-XIa
Inclusion Terms
  • Drug-induced hemorrhagic disorder
  • Hemorrhagic disorder due to increase in anti-IIa
  • Hemorrhagic disorder due to increase in anti-Xa
  • Hyperheparinemia
Inclusion Terms
  • Deficiency of coagulation factor due to liver disease
  • Deficiency of coagulation factor due to vitamin K deficiency
Inclusion Terms

Primary hypercoagulable states

Inclusion Terms

Factor V Leiden mutation

Inclusion Terms
  • Antithrombin III deficiency
  • Hypercoagulable state NOS
  • Primary hypercoagulable state NEC
  • Primary thrombophilia NEC
  • Protein C deficiency
  • Protein S deficiency
  • Thrombophilia NOS
Inclusion Terms

Other hypercoagulable states

Inclusion Terms
  • Anticardiolipin syndrome
  • Antiphospholipid antibody syndrome
Inclusion Terms
  • Lupus anticoagulant
  • Presence of systemic lupus erythematosus [SLE] inhibitor
Inclusion Terms
  • COVID-19 associated hypercoagulability
  • Hypercoagulable states NEC
  • Secondary hypercoagulable state NOS
Inclusion Terms

COVID-19 associated coagulopathy

Code Also

, if applicable, qualitative platelet defects (D69.1)

Code Also

, if applicable, associated condition

Code Also

, if applicable, associated condition

Child Codes (More Specific Codes for D68):

About ICD-10-CM Code D68 (Other coagulation defects)

ICD-10-CM code D68 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM D68 became effective on October 1, 2024.

This page provides detailed information about D68 - Other coagulation defects. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Other coagulation defects.