ICD-10-CM D68.0: Von Willebrand disease

ICD-10-CM Diagnosis Code (2025)

Official Description for D68.0

Von Willebrand disease

Coding Notes & Guidelines for D68.0

Excludes1: Not Coded Here
  • capillary fragility (hereditary) (D69.8)
  • factor VIII deficiency NOS (D66)
  • factor VIII deficiency with functional defect (D66)
Inclusion Terms
  • Partial quantitative deficiency of von Willebrand factor
  • Type 1C von Willebrand disease
Inclusion Terms

Qualitative defects of von Willebrand factor

Inclusion Terms

Qualitative defects of von Willebrand factor with decreased platelet adhesion and selective deficiency of high-molecular-weight multimers

Inclusion Terms
  • Qualitative defects of von Willebrand factor with high-molecular-weight von Willebrand factor loss
  • Qualitative defects of von Willebrand factor with hyper-adhesive forms
  • Qualitative defects of von Willebrand factor with increased affinity for platelet glycoprotein lb
Inclusion Terms

Qualitative defects of von Willebrand factor with defective platelet adhesion with a normal size distribution of von Willebrand factor multimers

Inclusion Terms
  • Qualitative defects of von Willebrand factor with defective von Willebrand factor to factor VIII binding
  • Qualitative defects of von Willebrand factor with markedly decreased affinity for factor VIII
Inclusion Terms

Qualitative defect in von Willebrand factor function, with no further subtyping

Inclusion Terms
  • (Near) complete absence of von Willebrand factor
  • Total quantitative deficiency of von Willebrand factor
Inclusion Terms

Acquired von Willebrand syndrome

Inclusion Terms
  • Platelet-type von Willebrand disease
  • Pseudo-von Willebrand disease
Code Also

, if applicable, qualitative platelet defects (D69.1)

Parent Code (Less Specific):

About ICD-10-CM Code D68.0 (Von Willebrand disease)

ICD-10-CM code D68.0 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM D68.0 became effective on October 1, 2024.

This page provides detailed information about D68.0 - Von Willebrand disease. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Von Willebrand disease.