ICD-10-CM D68.5: Primary thrombophilia

ICD-10-CM Diagnosis Code (2025)

Official Description for D68.5

Primary thrombophilia

Coding Notes & Guidelines for D68.5

Excludes1: Not Coded Here
  • antiphospholipid syndrome (D68.61)
  • lupus anticoagulant (D68.62)
  • secondary activated protein C resistance (D68.69)
  • secondary antiphospholipid antibody syndrome (D68.69)
  • secondary lupus anticoagulant with hypercoagulable state (D68.69)
  • secondary systemic lupus erythematosus [SLE] inhibitor with hypercoagulable state (D68.69)
  • systemic lupus erythematosus [SLE] inhibitor finding without diagnosis (R76.0)
  • systemic lupus erythematosus [SLE] inhibitor with hemorrhagic disorder (D68.312)
  • thrombotic thrombocytopenic purpura (M31.19)
Inclusion Terms

Primary hypercoagulable states

Inclusion Terms

Factor V Leiden mutation

Inclusion Terms
  • Antithrombin III deficiency
  • Hypercoagulable state NOS
  • Primary hypercoagulable state NEC
  • Primary thrombophilia NEC
  • Protein C deficiency
  • Protein S deficiency
  • Thrombophilia NOS

Parent Code (Less Specific):

About ICD-10-CM Code D68.5 (Primary thrombophilia)

ICD-10-CM code D68.5 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM D68.5 became effective on October 1, 2024.

This page provides detailed information about D68.5 - Primary thrombophilia. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Primary thrombophilia.