ICD-10-CM D70.0: Congenital agranulocytosis

ICD-10-CM Diagnosis Code (2025)

Official Description for D70.0

Congenital agranulocytosis

Coding Notes & Guidelines for D70.0

Inclusion Terms
  • Congenital neutropenia
  • Infantile genetic agranulocytosis
  • Kostmann's disease

Parent Code (Less Specific):

About ICD-10-CM Code D70.0 (Congenital agranulocytosis)

ICD-10-CM code D70.0 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM D70.0 became effective on October 1, 2024.

This page provides detailed information about D70.0 - Congenital agranulocytosis. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Congenital agranulocytosis.