ICD-10-CM Diagnosis Code (2025)
Official Description for D76.1
Hemophagocytic lymphohistiocytosis
Coding Notes & Guidelines for D76.1
Inclusion Terms
- Familial hemophagocytic reticulosis
- Histiocytoses of mononuclear phagocytes
Parent Code (Less Specific):
About ICD-10-CM Code D76.1 (Hemophagocytic lymphohistiocytosis)
ICD-10-CM code D76.1 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM D76.1 became effective on October 1, 2024.
This page provides detailed information about D76.1 - Hemophagocytic lymphohistiocytosis. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Hemophagocytic lymphohistiocytosis.