ICD-10-CM Diagnosis Code (2025)
Official Description for D80
Immunodeficiency with predominantly antibody defects
Coding Notes & Guidelines for D80
Inclusion Terms
- Autosomal recessive agammaglobulinemia (Swiss type)
- X-linked agammaglobulinemia [Bruton] (with growth hormone deficiency)
Inclusion Terms
- Agammaglobulinemia with immunoglobulin-bearing B-lymphocytes
- Common variable agammaglobulinemia [CVAgamma]
- Hypogammaglobulinemia NOS
Inclusion Terms
Kappa light chain deficiency
Child Codes (More Specific Codes for D80):
D80.0 - Hereditary hypogammaglobulinemia
D80.1 - Nonfamilial hypogammaglobulinemia
D80.2 - Selective deficiency of immunoglobulin A [IgA]
D80.3 - Selective deficiency of immunoglobulin G [IgG] subclasses
D80.4 - Selective deficiency of immunoglobulin M [IgM]
D80.5 - Immunodeficiency with increased immunoglobulin M [IgM]
D80.6 - Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia
D80.7 - Transient hypogammaglobulinemia of infancy
D80.8 - Other immunodeficiencies with predominantly antibody defects
D80.9 - Immunodeficiency with predominantly antibody defects, unspecified
About ICD-10-CM Code D80 (Immunodeficiency with predominantly antibody defects)
ICD-10-CM code D80 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM D80 became effective on October 1, 2024.
This page provides detailed information about D80 - Immunodeficiency with predominantly antibody defects. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Immunodeficiency with predominantly antibody defects.