ICD-10-CM D81.3: Adenosine deaminase [ADA] deficiency

ICD-10-CM Diagnosis Code (2025)

Official Description for D81.3

Adenosine deaminase [ADA] deficiency

Coding Notes & Guidelines for D81.3

Inclusion Terms

ADA deficiency NOS

Inclusion Terms
  • ADA deficiency with SCID
  • Adenosine deaminase [ADA] deficiency with severe combined immunodeficiency
Inclusion Terms
  • ADA2 deficiency
  • Adenosine deaminase deficiency type 2
Inclusion Terms
  • Adenosine deaminase [ADA] deficiency type 1, NOS
  • Adenosine deaminase [ADA] deficiency type 1, without SCID
  • Adenosine deaminase [ADA] deficiency type 1, without severe combined immunodeficiency
  • Partial ADA deficiency (type 1)
  • Partial adenosine deaminase deficiency (type 1)
Code Also
  • , if applicable, any associated manifestations, such as:
  • polyarteritis nodosa (M30.0)
  • stroke (I63.-)

Parent Code (Less Specific):

About ICD-10-CM Code D81.3 (Adenosine deaminase [ADA] deficiency)

ICD-10-CM code D81.3 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM D81.3 became effective on October 1, 2024.

This page provides detailed information about D81.3 - Adenosine deaminase [ADA] deficiency. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Adenosine deaminase [ADA] deficiency.