ICD-10-CM D81.31: Severe combined immunodeficiency due to adenosine deaminase deficiency

ICD-10-CM Diagnosis Code (2025)

Official Description for D81.31

Severe combined immunodeficiency due to adenosine deaminase deficiency

Coding Notes & Guidelines for D81.31

Inclusion Terms
  • ADA deficiency with SCID
  • Adenosine deaminase [ADA] deficiency with severe combined immunodeficiency

Parent Code (Less Specific):

About ICD-10-CM Code D81.31 (Severe combined immunodeficiency due to adenosine deaminase deficiency)

ICD-10-CM code D81.31 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM D81.31 became effective on October 1, 2024.

This page provides detailed information about D81.31 - Severe combined immunodeficiency due to adenosine deaminase deficiency. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Severe combined immunodeficiency due to adenosine deaminase deficiency.