ICD-10-CM Diagnosis Code (2025)
Official Description for D81.81
Biotin-dependent carboxylase deficiency
Coding Notes & Guidelines for D81.81
biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)
Multiple carboxylase deficiency
- Holocarboxylase synthetase deficiency
- Other multiple carboxylase deficiency
Multiple carboxylase deficiency, unspecified
Parent Code (Less Specific):
About ICD-10-CM Code D81.81 (Biotin-dependent carboxylase deficiency)
ICD-10-CM code D81.81 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM D81.81 became effective on October 1, 2024.
This page provides detailed information about D81.81 - Biotin-dependent carboxylase deficiency. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Biotin-dependent carboxylase deficiency.