ICD-10-CM E00: Congenital iodine-deficiency syndrome

ICD-10-CM Diagnosis Code (2025)

Official Description for E00

Congenital iodine-deficiency syndrome

Coding Notes & Guidelines for E00

Excludes1: Not Coded Here

subclinical iodine-deficiency hypothyroidism (E02)

Use Additional Code

code (F70-F79) to identify associated intellectual disabilities.

Inclusion Terms

Endemic cretinism, neurological type

Inclusion Terms
  • Endemic hypothyroid cretinism
  • Endemic cretinism, myxedematous type
Inclusion Terms

Endemic cretinism, mixed type

Inclusion Terms
  • Congenital iodine-deficiency hypothyroidism NOS
  • Endemic cretinism NOS

Child Codes (More Specific Codes for E00):

About ICD-10-CM Code E00 (Congenital iodine-deficiency syndrome)

ICD-10-CM code E00 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E00 became effective on October 1, 2024.

This page provides detailed information about E00 - Congenital iodine-deficiency syndrome. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Congenital iodine-deficiency syndrome.