ICD-10-CM E71.0: Maple-syrup-urine disease

Parent Code (Less Specific):

About ICD-10-CM Code E71.0 (Maple-syrup-urine disease)

ICD-10-CM code E71.0 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E71.0 became effective on October 1, 2024.

This page provides detailed information about E71.0 - Maple-syrup-urine disease. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Maple-syrup-urine disease.