ICD-10-CM E71.1: Other disorders of branched-chain amino-acid metabolism

ICD-10-CM Diagnosis Code (2025)

Official Description for E71.1

Other disorders of branched-chain amino-acid metabolism

Coding Notes & Guidelines for E71.1

Inclusion Terms
  • Hyperleucine-isoleucinemia
  • Hypervalinemia

Parent Code (Less Specific):

About ICD-10-CM Code E71.1 (Other disorders of branched-chain amino-acid metabolism)

ICD-10-CM code E71.1 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E71.1 became effective on October 1, 2024.

This page provides detailed information about E71.1 - Other disorders of branched-chain amino-acid metabolism. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Other disorders of branched-chain amino-acid metabolism.