ICD-10-CM Diagnosis Code (2025)
Official Description for E71.3
Disorders of fatty-acid metabolism
Coding Notes & Guidelines for E71.3
- peroxisomal disorders (E71.5)
- Refsum's disease (G60.1)
- Schilder's disease (G37.0)
glutaric aciduria (type 1) NOS (E72.3)
carnitine deficiency due to inborn error of metabolism (E71.42)
- LCAD deficiency
- VLCAD deficiency
MCAD deficiency
SCAD deficiency
- Glutaric aciduria type II A
- Glutaric aciduria type II B
- Glutaric aciduria type II C
Parent Code (Less Specific):
About ICD-10-CM Code E71.3 (Disorders of fatty-acid metabolism)
ICD-10-CM code E71.3 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E71.3 became effective on October 1, 2024.
This page provides detailed information about E71.3 - Disorders of fatty-acid metabolism. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Disorders of fatty-acid metabolism.