ICD-10-CM E71.311: Medium chain acyl CoA dehydrogenase deficiency

ICD-10-CM Diagnosis Code (2025)

Official Description for E71.311

Medium chain acyl CoA dehydrogenase deficiency

Coding Notes & Guidelines for E71.311

Inclusion Terms

MCAD deficiency

Parent Code (Less Specific):

About ICD-10-CM Code E71.311 (Medium chain acyl CoA dehydrogenase deficiency)

ICD-10-CM code E71.311 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E71.311 became effective on October 1, 2024.

This page provides detailed information about E71.311 - Medium chain acyl CoA dehydrogenase deficiency. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Medium chain acyl CoA dehydrogenase deficiency.