ICD-10-CM E71.4: Disorders of carnitine metabolism

ICD-10-CM Diagnosis Code (2025)

Official Description for E71.4

Disorders of carnitine metabolism

Coding Notes & Guidelines for E71.4

Excludes1: Not Coded Here

Muscle carnitine palmitoyltransferase deficiency (E71.314)

Inclusion Terms
  • Carnitine deficiency due to hemodialysis
  • Carnitine deficiency due to Valproic acid therapy
Code Also

associated inborn error or metabolism

Parent Code (Less Specific):

About ICD-10-CM Code E71.4 (Disorders of carnitine metabolism)

ICD-10-CM code E71.4 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E71.4 became effective on October 1, 2024.

This page provides detailed information about E71.4 - Disorders of carnitine metabolism. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Disorders of carnitine metabolism.