ICD-10-CM E72.2: Disorders of urea cycle metabolism

ICD-10-CM Diagnosis Code (2025)

Official Description for E72.2

Disorders of urea cycle metabolism

Coding Notes & Guidelines for E72.2

Excludes1: Not Coded Here

disorders of ornithine metabolism (E72.4)

Excludes1: Not Coded Here
  • hyperammonemia-hyperornithinemia-homocitrullinemia syndrome E72.4
  • transient hyperammonemia of newborn (P74.6)
Inclusion Terms

Hyperammonemia

Parent Code (Less Specific):

About ICD-10-CM Code E72.2 (Disorders of urea cycle metabolism)

ICD-10-CM code E72.2 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E72.2 became effective on October 1, 2024.

This page provides detailed information about E72.2 - Disorders of urea cycle metabolism. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Disorders of urea cycle metabolism.