ICD-10-CM E74: Other disorders of carbohydrate metabolism

ICD-10-CM Diagnosis Code (2025)

Official Description for E74

Other disorders of carbohydrate metabolism

Coding Notes & Guidelines for E74

Excludes1: Not Coded Here
  • diabetes mellitus (E08-E13)
  • hypoglycemia NOS (E16.2)
  • increased secretion of glucagon (E16.3)
  • mucopolysaccharidosis (E76.0-E76.3)
Excludes1: Not Coded Here

muscle phosphofructokinase deficiency (E74.09)

Excludes1: Not Coded Here
  • disorders of pyruvate metabolism and gluconeogenesis with anemia (D55.-)
  • Leigh's syndrome (G31.82)
Excludes2: Not Included Here

lactose intolerance (E73.-)

Inclusion Terms

Type I glycogen storage disease

Inclusion Terms
  • Cardiac glycogenosis
  • Type II glycogen storage disease
Inclusion Terms
  • Forbes disease
  • Type III glycogen storage disease
Inclusion Terms

Type V glycogen storage disease

Inclusion Terms

Danon disease

Inclusion Terms
  • Andersen disease
  • Glycogen storage disease, types 0, IV, VI-XI
  • Hers disease
  • Liver phosphorylase deficiency
  • Muscle phosphofructokinase deficiency
  • Tauri disease
Inclusion Terms

Fructokinase deficiency

Inclusion Terms

Fructosemia

Inclusion Terms

Fructose-1, 6-diphosphatase deficiency

Inclusion Terms

Galactokinase deficiency

Inclusion Terms
  • Disorder of intestinal carbohydrate absorption NOS
  • Glucose-galactose malabsorption
  • Sucrase deficiency
Inclusion Terms
  • Deficiency of phosphoenolpyruvate carboxykinase
  • Deficiency of pyruvate carboxylase
  • Deficiency of pyruvate dehydrogenase
Inclusion Terms
  • De Vivo syndrome
  • Glucose transport defect, blood-brain barrier
  • Glut1 deficiency
  • GLUT1 deficiency syndrome 1, infantile onset
  • GLUT1 deficiency syndrome 2, childhood onset
Inclusion Terms

(Familial) renal glycosuria

Inclusion Terms

Essential pentosuria

Code Also
  • , if applicable, associated manifestations such as:
  • dilated cardiomyopathy (I42.0)
  • obstructive hypertrophic cardiomyopathy (I42.1)

Child Codes (More Specific Codes for E74):

About ICD-10-CM Code E74 (Other disorders of carbohydrate metabolism)

ICD-10-CM code E74 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E74 became effective on October 1, 2024.

This page provides detailed information about E74 - Other disorders of carbohydrate metabolism. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Other disorders of carbohydrate metabolism.