ICD-10-CM E75.2: Other sphingolipidosis

ICD-10-CM Diagnosis Code (2025)

Official Description for E75.2

Other sphingolipidosis

Coding Notes & Guidelines for E75.2

Excludes1: Not Coded Here

adrenoleukodystrophy [Addison-Schilder] (E71.528)

Inclusion Terms

Acid sphingomyelinase deficiency (ASMD)

Inclusion Terms
  • Acid sphingomyelinase deficiency type A (ASMD type A)
  • Infantile neurovisceral acid sphingomyelinase deficiency
Inclusion Terms
  • Acid sphingomyelinase deficiency type B (ASMD type B)
  • Chronic visceral acid sphingomyelinase deficiency
Inclusion Terms
  • Acid sphingomyelinase deficiency type A/B (ASMD type A/B)
  • Chronic neurovisceral acid sphingomyelinase deficiency
Inclusion Terms

Acid sphingomyelinase deficiency (ASMD) NOS

Inclusion Terms

Multiple sulfatase deficiency (MSD)

Inclusion Terms
  • Farber's syndrome
  • Sulfatide lipidosis

Parent Code (Less Specific):

About ICD-10-CM Code E75.2 (Other sphingolipidosis)

ICD-10-CM code E75.2 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E75.2 became effective on October 1, 2024.

This page provides detailed information about E75.2 - Other sphingolipidosis. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Other sphingolipidosis.