ICD-10-CM E75.241: Niemann-Pick disease type B

ICD-10-CM Diagnosis Code (2025)

Official Description for E75.241

Niemann-Pick disease type B

Coding Notes & Guidelines for E75.241

Inclusion Terms
  • Acid sphingomyelinase deficiency type B (ASMD type B)
  • Chronic visceral acid sphingomyelinase deficiency

Parent Code (Less Specific):

About ICD-10-CM Code E75.241 (Niemann-Pick disease type B)

ICD-10-CM code E75.241 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E75.241 became effective on October 1, 2024.

This page provides detailed information about E75.241 - Niemann-Pick disease type B. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Niemann-Pick disease type B.