ICD-10-CM E75.249: Niemann-Pick disease, unspecified

ICD-10-CM Diagnosis Code (2025)

Official Description for E75.249

Niemann-Pick disease, unspecified

Coding Notes & Guidelines for E75.249

Inclusion Terms

Acid sphingomyelinase deficiency (ASMD) NOS

Parent Code (Less Specific):

About ICD-10-CM Code E75.249 (Niemann-Pick disease)

ICD-10-CM code E75.249 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E75.249 became effective on October 1, 2024.

This page provides detailed information about E75.249 - Niemann-Pick disease, unspecified. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Niemann-Pick disease related to unspecified.