ICD-10-CM E76: Disorders of glycosaminoglycan metabolism

ICD-10-CM Diagnosis Code (2025)

Official Description for E76

Disorders of glycosaminoglycan metabolism

Coding Notes & Guidelines for E76

Inclusion Terms

Hunter's syndrome

Inclusion Terms
  • Classic Morquio syndrome
  • Morquio syndrome A
  • Mucopolysaccharidosis, type IVA
Inclusion Terms
  • Morquio-like mucopolysaccharidoses
  • Morquio-like syndrome
  • Morquio syndrome B
  • Mucopolysaccharidosis, type IVB
Inclusion Terms
  • Morquio syndrome
  • Mucopolysaccharidosis, type IV
Inclusion Terms
  • Mucopolysaccharidosis, type III (A) (B) (C) (D)
  • Sanfilippo A syndrome
  • Sanfilippo B syndrome
  • Sanfilippo C syndrome
  • Sanfilippo D syndrome
Inclusion Terms
  • beta-Glucuronidase deficiency
  • Maroteaux-Lamy (mild) (severe) syndrome
  • Mucopolysaccharidosis, types VI, VII

Child Codes (More Specific Codes for E76):

E76.0 - Mucopolysaccharidosis, type I E76.01 - Hurler's syndrome E76.02 - Hurler-Scheie syndrome E76.03 - Scheie's syndrome E76.1 - Mucopolysaccharidosis, type II E76.2 - Other mucopolysaccharidoses E76.21 - Morquio mucopolysaccharidoses E76.210 - Morquio A mucopolysaccharidoses E76.211 - Morquio B mucopolysaccharidoses E76.219 - Morquio mucopolysaccharidoses, unspecified E76.22 - Sanfilippo mucopolysaccharidoses E76.29 - Other mucopolysaccharidoses E76.3 - Mucopolysaccharidosis, unspecified E76.8 - Other disorders of glucosaminoglycan metabolism E76.9 - Glucosaminoglycan metabolism disorder, unspecified

About ICD-10-CM Code E76 (Disorders of glycosaminoglycan metabolism)

ICD-10-CM code E76 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E76 became effective on October 1, 2024.

This page provides detailed information about E76 - Disorders of glycosaminoglycan metabolism. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Disorders of glycosaminoglycan metabolism.