ICD-10-CM E76.2: Other mucopolysaccharidoses

ICD-10-CM Diagnosis Code (2025)

Official Description for E76.2

Other mucopolysaccharidoses

Coding Notes & Guidelines for E76.2

Inclusion Terms
  • Classic Morquio syndrome
  • Morquio syndrome A
  • Mucopolysaccharidosis, type IVA
Inclusion Terms
  • Morquio-like mucopolysaccharidoses
  • Morquio-like syndrome
  • Morquio syndrome B
  • Mucopolysaccharidosis, type IVB
Inclusion Terms
  • Morquio syndrome
  • Mucopolysaccharidosis, type IV
Inclusion Terms
  • Mucopolysaccharidosis, type III (A) (B) (C) (D)
  • Sanfilippo A syndrome
  • Sanfilippo B syndrome
  • Sanfilippo C syndrome
  • Sanfilippo D syndrome
Inclusion Terms
  • beta-Glucuronidase deficiency
  • Maroteaux-Lamy (mild) (severe) syndrome
  • Mucopolysaccharidosis, types VI, VII

Parent Code (Less Specific):

About ICD-10-CM Code E76.2 (Other mucopolysaccharidoses)

ICD-10-CM code E76.2 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E76.2 became effective on October 1, 2024.

This page provides detailed information about E76.2 - Other mucopolysaccharidoses. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Other mucopolysaccharidoses.