ICD-10-CM Diagnosis Code (2025)
Official Description for E76.22
Sanfilippo mucopolysaccharidoses
Coding Notes & Guidelines for E76.22
Inclusion Terms
- Mucopolysaccharidosis, type III (A) (B) (C) (D)
- Sanfilippo A syndrome
- Sanfilippo B syndrome
- Sanfilippo C syndrome
- Sanfilippo D syndrome
Parent Code (Less Specific):
About ICD-10-CM Code E76.22 (Sanfilippo mucopolysaccharidoses)
ICD-10-CM code E76.22 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E76.22 became effective on October 1, 2024.
This page provides detailed information about E76.22 - Sanfilippo mucopolysaccharidoses. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Sanfilippo mucopolysaccharidoses.