ICD-10-CM Diagnosis Code (2025)
Official Description for E77.0
Defects in post-translational modification of lysosomal enzymes
Coding Notes & Guidelines for E77.0
- Mucolipidosis II [I-cell disease]
- Mucolipidosis III [pseudo-Hurler polydystrophy]
Parent Code (Less Specific):
About ICD-10-CM Code E77.0 (Defects in post-translational modification of lysosomal enzymes)
ICD-10-CM code E77.0 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E77.0 became effective on October 1, 2024.
This page provides detailed information about E77.0 - Defects in post-translational modification of lysosomal enzymes. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Defects in post-translational modification of lysosomal enzymes.