ICD-10-CM E79.1: Lesch-Nyhan syndrome

ICD-10-CM Diagnosis Code (2025)

Official Description for E79.1

Lesch-Nyhan syndrome

Coding Notes & Guidelines for E79.1

Inclusion Terms

HGPRT deficiency

Parent Code (Less Specific):

About ICD-10-CM Code E79.1 (Lesch-Nyhan syndrome)

ICD-10-CM code E79.1 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E79.1 became effective on October 1, 2024.

This page provides detailed information about E79.1 - Lesch-Nyhan syndrome. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Lesch-Nyhan syndrome.