ICD-10-CM E80: Disorders of porphyrin and bilirubin metabolism

ICD-10-CM Diagnosis Code (2025)

Official Description for E80

Disorders of porphyrin and bilirubin metabolism

Coding Notes & Guidelines for E80

Includes Notes

defects of catalase and peroxidase

Inclusion Terms
  • Congenital erythropoietic porphyria
  • Erythropoietic protoporphyria
Inclusion Terms

Porphyria NOS

Inclusion Terms

Hereditary coproporphyria

Inclusion Terms

Acatalasia [Takahara]

Inclusion Terms
  • Dubin-Johnson syndrome
  • Rotor's syndrome

Child Codes (More Specific Codes for E80):

E80.0 - Hereditary erythropoietic porphyria E80.1 - Porphyria cutanea tarda E80.2 - Other and unspecified porphyria E80.20 - Unspecified porphyria E80.21 - Acute intermittent (hepatic) porphyria E80.29 - Other porphyria E80.3 - Defects of catalase and peroxidase E80.4 - Gilbert syndrome E80.5 - Crigler-Najjar syndrome E80.6 - Other disorders of bilirubin metabolism E80.7 - Disorder of bilirubin metabolism, unspecified

About ICD-10-CM Code E80 (Disorders of porphyrin and bilirubin metabolism)

ICD-10-CM code E80 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E80 became effective on October 1, 2024.

This page provides detailed information about E80 - Disorders of porphyrin and bilirubin metabolism. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Disorders of porphyrin and bilirubin metabolism.