ICD-10-CM E80.0: Hereditary erythropoietic porphyria

ICD-10-CM Diagnosis Code (2025)

Official Description for E80.0

Hereditary erythropoietic porphyria

Coding Notes & Guidelines for E80.0

Inclusion Terms
  • Congenital erythropoietic porphyria
  • Erythropoietic protoporphyria

Parent Code (Less Specific):

About ICD-10-CM Code E80.0 (Hereditary erythropoietic porphyria)

ICD-10-CM code E80.0 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E80.0 became effective on October 1, 2024.

This page provides detailed information about E80.0 - Hereditary erythropoietic porphyria. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Hereditary erythropoietic porphyria.