ICD-10-CM Diagnosis Code (2025)
Official Description for E88.0
Disorders of plasma-protein metabolism, not elsewhere classified
Coding Notes & Guidelines for E88.0
- monoclonal gammopathy (of undetermined significance) (D47.2)
- polyclonal hypergammaglobulinemia (D89.0)
- Waldenström macroglobulinemia (C88.00)
disorder of lipoprotein metabolism (E78.-)
- code for associated findings, such as:
- hydrocephalus (G91.4)
- otitis media (H67.-)
- respiratory disorder related to plasminogen deficiency (J99)
AAT deficiency
- Dysplasminogenemia
- Hypoplasminogenemia
- Type 1 plasminogen deficiency
- Type 2 plasminogen deficiency
Bisalbuminemia
, if applicable, ligneous conjunctivitis (H10.51)
Parent Code (Less Specific):
About ICD-10-CM Code E88.0 (Disorders of plasma-protein metabolism)
ICD-10-CM code E88.0 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E88.0 became effective on October 1, 2024.
This page provides detailed information about E88.0 - Disorders of plasma-protein metabolism, not elsewhere classified. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Disorders of plasma-protein metabolism related to not elsewhere classified.