ICD-10-CM Diagnosis Code (2025)
Official Description for E88.4
Mitochondrial metabolism disorders
Coding Notes & Guidelines for E88.4
- disorders of pyruvate metabolism (E74.4)
- Kearns-Sayre syndrome (H49.81)
- Leber's disease (H47.22)
- Leigh's encephalopathy (G31.82)
- Mitochondrial myopathy, NEC (G71.3)
- Reye's syndrome (G93.7)
Mitochondrial myopathy, encephalopathy, lactic acidosis and stroke-like episodes
Myoclonic epilepsy associated with ragged-red fibers
progressive myoclonic epilepsy (G40.3-)
Parent Code (Less Specific):
About ICD-10-CM Code E88.4 (Mitochondrial metabolism disorders)
ICD-10-CM code E88.4 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E88.4 became effective on October 1, 2024.
This page provides detailed information about E88.4 - Mitochondrial metabolism disorders. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Mitochondrial metabolism disorders.