ICD-10-CM E88.40: Mitochondrial metabolism disorder, unspecified

ICD-10-CM Diagnosis Code (2025)

Official Description for E88.40

Mitochondrial metabolism disorder, unspecified

Parent Code (Less Specific):

About ICD-10-CM Code E88.40 (Mitochondrial metabolism disorder)

ICD-10-CM code E88.40 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E88.40 became effective on October 1, 2024.

This page provides detailed information about E88.40 - Mitochondrial metabolism disorder, unspecified. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Mitochondrial metabolism disorder related to unspecified.