ICD-10-CM E88.42: MERRF syndrome

ICD-10-CM Diagnosis Code (2025)

Official Description for E88.42

MERRF syndrome

Coding Notes & Guidelines for E88.42

Inclusion Terms

Myoclonic epilepsy associated with ragged-red fibers

Code Also

progressive myoclonic epilepsy (G40.3-)

Parent Code (Less Specific):

About ICD-10-CM Code E88.42 (MERRF syndrome)

ICD-10-CM code E88.42 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM E88.42 became effective on October 1, 2024.

This page provides detailed information about E88.42 - MERRF syndrome. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like MERRF syndrome.