ICD-10-CM G11: Hereditary ataxia

ICD-10-CM Diagnosis Code (2025)

Official Description for G11

Hereditary ataxia

Coding Notes & Guidelines for G11

Excludes2: Not Included Here
  • cerebral palsy (G80.-)
  • hereditary and idiopathic neuropathy (G60.-)
  • metabolic disorders (E70-E88)
Excludes2: Not Included Here
  • Cockayne's syndrome (Q87.19)
  • other disorders of purine and pyrimidine metabolism (E79.-)
  • xeroderma pigmentosum (Q82.1)
Inclusion Terms
  • Autosomal recessive Friedreich ataxia
  • Friedreich ataxia with retained reflexes
Inclusion Terms
  • Early-onset cerebellar ataxia with essential tremor
  • Early-onset cerebellar ataxia with myoclonus [Hunt's ataxia]
  • Early-onset cerebellar ataxia with retained tendon reflexes
  • X-linked recessive spinocerebellar ataxia
Inclusion Terms

Ataxia telangiectasia [Louis-Bar]

Inclusion Terms
  • 4H syndrome
  • Pol III-related leukodystrophy
Inclusion Terms
  • Hereditary cerebellar ataxia NOS
  • Hereditary cerebellar degeneration
  • Hereditary cerebellar disease
  • Hereditary cerebellar syndrome

Child Codes (More Specific Codes for G11):

G11.0 - Congenital nonprogressive ataxia G11.1 - Early-onset cerebellar ataxia G11.10 - Early-onset cerebellar ataxia, unspecified G11.11 - Friedreich ataxia G11.19 - Other early-onset cerebellar ataxia G11.2 - Late-onset cerebellar ataxia G11.3 - Cerebellar ataxia with defective DNA repair G11.4 - Hereditary spastic paraplegia G11.5 - Hypomyelination - hypogonadotropic hypogonadism - hypodontia G11.6 - Leukodystrophy with vanishing white matter disease G11.8 - Other hereditary ataxias G11.9 - Hereditary ataxia, unspecified

About ICD-10-CM Code G11 (Hereditary ataxia)

ICD-10-CM code G11 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM G11 became effective on October 1, 2024.

This page provides detailed information about G11 - Hereditary ataxia. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Hereditary ataxia.