ICD-10-CM G71: Primary disorders of muscles

ICD-10-CM Diagnosis Code (2025)

Official Description for G71

Primary disorders of muscles

Coding Notes & Guidelines for G71

Excludes1: Not Coded Here
  • Kearns-Sayre syndrome (H49.81)
  • Leber's disease (H47.21)
  • Leigh's encephalopathy (G31.82)
  • mitochondrial metabolism disorders (E88.4.-)
  • Reye's syndrome (G93.7)
Excludes2: Not Included Here
  • arthrogryposis multiplex congenita (Q74.3)
  • metabolic disorders (E70-E88)
  • myositis (M60.-)
Excludes2: Not Included Here

arthrogryposis multiplex congenita (Q74.3)

Use Additional Code

code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)

Inclusion Terms
  • Autosomal recessive, childhood type, muscular dystrophy resembling Duchenne or Becker muscular dystrophy
  • Benign [Becker] muscular dystrophy
  • Severe [Duchenne] muscular dystrophy
Inclusion Terms

Scapulohumeral muscular dystrophy

Inclusion Terms
  • LGMD D4 calpain-3-related
  • LGMD D5 collagen 6-related
  • Limb girdle muscular dystrophy type 1
Inclusion Terms
  • Limb girdle muscular dystrophy type 2A
  • LGMD R1 calpain-3-related
  • Primary calpainopathy
Inclusion Terms
  • Dysferlinopathy
  • LGMD R2 dysferlin-related
  • Limb girdle muscular dystrophy type 2B
  • Miyoshi Myopathy type 1
Inclusion Terms

Sarcoglycanopathy, NOS

Inclusion Terms
  • Alpha sarcoglycanopathy
  • Limb-girdle muscular dystrophy due to alpha-sarcoglycan deficiency
  • Limb girdle muscular dystrophy type 2D
Inclusion Terms
  • Beta sarcoglycanopathy
  • Limb girdle muscular dystrophy due to beta-sarcoglycan deficiency
  • Limb girdle muscular dystrophy type 2E
Inclusion Terms
  • Delta sarcoglycanopathy
  • Delta-sarcoglycan-related LGMD R6
  • Gamma sarcoglycanopathy
  • Gamma-sarcoglycan-related LGMD R5
  • Limb girdle muscular dystrophy type 2C
  • Limb girdle muscular dystrophy type 2F
Inclusion Terms
  • Anoctamin-5-related LGMD R12
  • Anoctaminopathy
  • Autosomal recessive limb girdle muscular dystrophy type 2L
  • Miyoshi myopathy type 3
Inclusion Terms
  • LGMD R9 FKRP-related
  • LGMD R22 collagen 6-related
  • Limb girdle muscular dystrophy due to fukutin related protein dysfunction
  • Limb girdle muscular dystrophy type 2I
  • Other autosomal recessive limb girdle muscular dystrophy
Inclusion Terms
  • Benign scapuloperoneal muscular dystrophy with early contractures [Emery-Dreifuss]
  • Congenital muscular dystrophy NOS
  • Congenital muscular dystrophy with specific morphological abnormalities of the muscle fiber
  • Distal muscular dystrophy
  • Ocular muscular dystrophy
  • Oculopharyngeal muscular dystrophy
  • Scapuloperoneal muscular dystrophy
Inclusion Terms
  • Dystrophia myotonica [Steinert]
  • Myotonia atrophica
  • Myotonic dystrophy
  • Proximal myotonic myopathy (PROMM)
  • Steinert disease
Inclusion Terms
  • Acetazolamide responsive myotonia congenita
  • Dominant myotonia congenita [Thomsen disease]
  • Myotonia levior
  • Recessive myotonia congenita [Becker disease]
Inclusion Terms
  • Chondrodystrophic myotonia
  • Congenital myotonic chondrodystrophy
  • Schwartz-Jampel disease
Inclusion Terms
  • Myotonia fluctuans
  • Myotonia permanens
  • Neuromyotonia [Isaacs]
  • Paramyotonia congenita (of von Eulenburg)
  • Pseudomyotonia
  • Symptomatic myotonia
Inclusion Terms

Myotubular (centronuclear) myopathy

Inclusion Terms
  • Autosomal centronuclear myopathy
  • Autosomal dominant centronuclear myopathy
  • Autosomal recessive centronuclear myopathy
  • Centronuclear myopathy, NOS
Inclusion Terms
  • Central core disease
  • Minicore disease
  • Multicore disease
  • Multiminicore disease
Inclusion Terms

Hereditary myopathy NOS

Child Codes (More Specific Codes for G71):

G71.0 - Muscular dystrophy G71.00 - Muscular dystrophy, unspecified G71.01 - Duchenne or Becker muscular dystrophy G71.02 - Facioscapulohumeral muscular dystrophy G71.03 - Limb girdle muscular dystrophies G71.031 - Autosomal dominant limb girdle muscular dystrophy G71.032 - Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction G71.033 - Limb girdle muscular dystrophy due to dysferlin dysfunction G71.034 - Limb girdle muscular dystrophy due to sarcoglycan dysfunction G71.0340 - Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified G71.0341 - Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction G71.0342 - Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction G71.0349 - Limb girdle muscular dystrophy due to other sarcoglycan dysfunction G71.035 - Limb girdle muscular dystrophy due to anoctamin-5 dysfunction G71.038 - Other limb girdle muscular dystrophy G71.039 - Limb girdle muscular dystrophy, unspecified G71.09 - Other specified muscular dystrophies G71.1 - Myotonic disorders G71.11 - Myotonic muscular dystrophy G71.12 - Myotonia congenita G71.13 - Myotonic chondrodystrophy G71.14 - Drug induced myotonia G71.19 - Other specified myotonic disorders G71.2 - Congenital myopathies G71.20 - Congenital myopathy, unspecified G71.21 - Nemaline myopathy G71.22 - Centronuclear myopathy G71.220 - X-linked myotubular myopathy G71.228 - Other centronuclear myopathy G71.29 - Other congenital myopathy G71.3 - Mitochondrial myopathy, not elsewhere classified G71.8 - Other primary disorders of muscles G71.9 - Primary disorder of muscle, unspecified

About ICD-10-CM Code G71 (Primary disorders of muscles)

ICD-10-CM code G71 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM G71 became effective on October 1, 2024.

This page provides detailed information about G71 - Primary disorders of muscles. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Primary disorders of muscles.