ICD-10-CM G71.03: Limb girdle muscular dystrophies

ICD-10-CM Diagnosis Code (2025)

Official Description for G71.03

Limb girdle muscular dystrophies

Coding Notes & Guidelines for G71.03

Inclusion Terms
  • LGMD D4 calpain-3-related
  • LGMD D5 collagen 6-related
  • Limb girdle muscular dystrophy type 1
Inclusion Terms
  • Limb girdle muscular dystrophy type 2A
  • LGMD R1 calpain-3-related
  • Primary calpainopathy
Inclusion Terms
  • Dysferlinopathy
  • LGMD R2 dysferlin-related
  • Limb girdle muscular dystrophy type 2B
  • Miyoshi Myopathy type 1
Inclusion Terms

Sarcoglycanopathy, NOS

Inclusion Terms
  • Alpha sarcoglycanopathy
  • Limb-girdle muscular dystrophy due to alpha-sarcoglycan deficiency
  • Limb girdle muscular dystrophy type 2D
Inclusion Terms
  • Beta sarcoglycanopathy
  • Limb girdle muscular dystrophy due to beta-sarcoglycan deficiency
  • Limb girdle muscular dystrophy type 2E
Inclusion Terms
  • Delta sarcoglycanopathy
  • Delta-sarcoglycan-related LGMD R6
  • Gamma sarcoglycanopathy
  • Gamma-sarcoglycan-related LGMD R5
  • Limb girdle muscular dystrophy type 2C
  • Limb girdle muscular dystrophy type 2F
Inclusion Terms
  • Anoctamin-5-related LGMD R12
  • Anoctaminopathy
  • Autosomal recessive limb girdle muscular dystrophy type 2L
  • Miyoshi myopathy type 3
Inclusion Terms
  • LGMD R9 FKRP-related
  • LGMD R22 collagen 6-related
  • Limb girdle muscular dystrophy due to fukutin related protein dysfunction
  • Limb girdle muscular dystrophy type 2I
  • Other autosomal recessive limb girdle muscular dystrophy

Parent Code (Less Specific):

G71 - Primary disorders of muscles

About ICD-10-CM Code G71.03 (Limb girdle muscular dystrophies)

ICD-10-CM code G71.03 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM G71.03 became effective on October 1, 2024.

This page provides detailed information about G71.03 - Limb girdle muscular dystrophies. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Limb girdle muscular dystrophies.