ICD-10-CM G71.3: Mitochondrial myopathy, not elsewhere classified

ICD-10-CM Diagnosis Code (2025)

Official Description for G71.3

Mitochondrial myopathy, not elsewhere classified

Coding Notes & Guidelines for G71.3

Excludes1: Not Coded Here
  • Kearns-Sayre syndrome (H49.81)
  • Leber's disease (H47.21)
  • Leigh's encephalopathy (G31.82)
  • mitochondrial metabolism disorders (E88.4.-)
  • Reye's syndrome (G93.7)

Parent Code (Less Specific):

About ICD-10-CM Code G71.3 (Mitochondrial myopathy)

ICD-10-CM code G71.3 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM G71.3 became effective on October 1, 2024.

This page provides detailed information about G71.3 - Mitochondrial myopathy, not elsewhere classified. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Mitochondrial myopathy related to not elsewhere classified.