ICD-10-CM G91: Hydrocephalus

ICD-10-CM Diagnosis Code (2025)

Official Description for G91

Hydrocephalus

Coding Notes & Guidelines for G91

Includes Notes

acquired hydrocephalus

Excludes1: Not Coded Here
  • Arnold-Chiari syndrome with hydrocephalus (Q07.-)
  • congenital hydrocephalus (Q03.-)
  • spina bifida with hydrocephalus (Q05.-)
Excludes1: Not Coded Here

hydrocephalus due to congenital toxoplasmosis (P37.1)

Code First
  • underlying condition, such as:
  • congenital syphilis (A50.4-)
  • neoplasm (C00-D49)
  • plasminogen deficiency (E88.02)
Inclusion Terms

Secondary normal pressure hydrocephalus

Inclusion Terms

Normal pressure hydrocephalus NOS

Child Codes (More Specific Codes for G91):

About ICD-10-CM Code G91 (Hydrocephalus)

ICD-10-CM code G91 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM G91 became effective on October 1, 2024.

This page provides detailed information about G91 - Hydrocephalus. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Hydrocephalus.