ICD-10-CM H49.81: Kearns-Sayre syndrome

ICD-10-CM Diagnosis Code (2025)

Official Description for H49.81

Kearns-Sayre syndrome

Coding Notes & Guidelines for H49.81

Inclusion Terms

Progressive external ophthalmoplegia with pigmentary retinopathy

Code Also
  • , if applicable, other manifestations, such as:
  • heart block (I45.9)

Parent Code (Less Specific):

About ICD-10-CM Code H49.81 (Kearns-Sayre syndrome)

ICD-10-CM code H49.81 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM H49.81 became effective on October 1, 2024.

This page provides detailed information about H49.81 - Kearns-Sayre syndrome. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Kearns-Sayre syndrome.