ICD-10-CM I01: Rheumatic fever with heart involvement

ICD-10-CM Diagnosis Code (2025)

Official Description for I01

Rheumatic fever with heart involvement

Coding Notes & Guidelines for I01

Excludes1: Not Coded Here

chronic diseases of rheumatic origin (I05-I09) unless rheumatic fever is also present or there is evidence of reactivation or activity of the rheumatic process.

Excludes1: Not Coded Here

acute pericarditis not specified as rheumatic (I30.-)

Inclusion Terms
  • Any condition in I00 with pericarditis
  • Rheumatic pericarditis (acute)
Inclusion Terms
  • Any condition in I00 with endocarditis or valvulitis
  • Acute rheumatic valvulitis
Inclusion Terms

Any condition in I00 with myocarditis

Inclusion Terms
  • Any condition in I00 with other or multiple types of heart involvement
  • Acute rheumatic pancarditis
Inclusion Terms
  • Any condition in I00 with unspecified type of heart involvement
  • Rheumatic carditis, acute
  • Rheumatic heart disease, active or acute

Child Codes (More Specific Codes for I01):

About ICD-10-CM Code I01 (Rheumatic fever with heart involvement)

ICD-10-CM code I01 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM I01 became effective on October 1, 2024.

This page provides detailed information about I01 - Rheumatic fever with heart involvement. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Rheumatic fever with heart involvement.