ICD-10-CM I27: Other pulmonary heart diseases

• persistent pulmonary hypertension of newborn (P29.30)
• pulmonary hypertension NOS (I27.20)
• secondary pulmonary arterial hypertension (I27.21)
• secondary pulmonary hypertension (I27.29)

Eisenmenger's syndrome (I27.83)

acute cor pulmonale (I26.0-)

personal history of pulmonary embolism (Z86.711)

code, if applicable, for associated long-term (current) use of anticoagulants (Z79.01)

• Heritable pulmonary arterial hypertension
• Idiopathic pulmonary arterial hypertension
• Primary group 1 pulmonary hypertension
• Primary pulmonary arterial hypertension

Pulmonary hypertension NOS

• (Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS
• (Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension

Group 2 pulmonary hypertension

Group 3 pulmonary hypertension

Group 4 pulmonary hypertension

• Group 5 pulmonary hypertension
• Pulmonary hypertension with unclear multifactorial mechanisms
• Pulmonary hypertension due to hematologic disorders
• Pulmonary hypertension due to metabolic disorders
• Pulmonary hypertension due to other systemic disorders

Cor pulmonale NOS

• Eisenmenger's complex
• (Irreversible) Eisenmenger's disease
• Pulmonary hypertension with right to left shunt related to congenital heart disease

Chronic cardiopulmonary disease

associated underlying condition

• associated conditions if applicable, or adverse effects of drugs or toxins, such as:
• adverse effect of appetite depressants (T50.5X5)
• congenital heart disease (Q20-Q28)
• human immunodeficiency virus [HIV] disease (B20)
• polymyositis (M33.2-)
• portal hypertension (K76.6)
• rheumatoid arthritis (M05.-)
• schistosomiasis (B65.-)
• Sjögren syndrome (M35.0-)
• systemic sclerosis (M34.-)

• associated left heart disease, if known, such as:
• multiple valve disease (I08.-)
• rheumatic mitral valve diseases (I05.-)
• rheumatic aortic valve diseases (I06.-)

• associated lung disease, if known, such as:
• bronchiectasis (J47.-)
• cystic fibrosis with pulmonary manifestations (E84.0)
• interstitial lung disease (J84.-)
• pleural effusion (J90)
• sleep apnea (G47.3-)

associated pulmonary embolism, if applicable (I26.-, I27.82)

• other associated disorders, if known, such as:
• chronic myeloid leukemia (C92.10-C92.22)
• essential thrombocythemia (D47.3)
• Gaucher disease (E75.22)
• hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
• hyperthyroidism (E05.-)
• hypothyroidism (E00-E03)
• polycythemia vera (D45)
• sarcoidosis (D86.-)

, if applicable, right heart failure (I50.81-)

• underlying heart defect, if known, such as:
• atrial septal defect (Q21.1-)
• Eisenmenger's defect (Q21.8)
• patent ductus arteriosus (Q25.0)
• ventricular septal defect (Q21.0)