ICD-10-CM J43.0: Unilateral pulmonary emphysema [MacLeod's syndrome]

ICD-10-CM Diagnosis Code (2025)

Official Description for J43.0

Unilateral pulmonary emphysema [MacLeod's syndrome]

Coding Notes & Guidelines for J43.0

Inclusion Terms
  • Swyer-James syndrome
  • Unilateral emphysema
  • Unilateral hyperlucent lung
  • Unilateral pulmonary artery functional hypoplasia
  • Unilateral transparency of lung

Parent Code (Less Specific):

About ICD-10-CM Code J43.0 (Unilateral pulmonary emphysema [MacLeod's syndrome])

ICD-10-CM code J43.0 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM J43.0 became effective on October 1, 2024.

This page provides detailed information about J43.0 - Unilateral pulmonary emphysema [MacLeod's syndrome]. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Unilateral pulmonary emphysema [MacLeod's syndrome].