ICD-10-CM J84: Other interstitial pulmonary diseases

ICD-10-CM Diagnosis Code (2025)

Official Description for J84

Other interstitial pulmonary diseases

Coding Notes & Guidelines for J84

Excludes1: Not Coded Here
  • drug-induced interstitial lung disorders (J70.2-J70.4)
  • interstitial emphysema (J98.2)
Excludes1: Not Coded Here

acute idiopathic pulmonary hemorrhage in infants [AIPHI] (R04.81)

Excludes1: Not Coded Here
  • pulmonary fibrosis (chronic) due to inhalation of chemicals, gases, fumes or vapors (J68.4)
  • pulmonary fibrosis (chronic) following radiation (J70.1)
Excludes1: Not Coded Here
  • lymphoid interstitial pneumonia (J84.2)
  • pneumocystis pneumonia (B59)
Excludes1: Not Coded Here

non-specific interstitial pneumonia NOS, or due to known underlying cause (J84.89)

Excludes1: Not Coded Here

pneumocystis pneumonia (B59)

Excludes1: Not Coded Here

organizing pneumonia NOS, or due to known underlying cause (J84.89)

Excludes1: Not Coded Here
  • exogenous lipoid pneumonia (J69.1)
  • unspecified lipoid pneumonia (J69.1)
Excludes1: Not Coded Here
  • cryptogenic organizing pneumonia (J84.116)
  • idiopathic non-specific interstitial pneumonitis (J84.113)
  • lipoid pneumonia, exogenous or unspecified (J69.1)
  • lymphoid interstitial pneumonia (J84.2)
Excludes2: Not Included Here

lung diseases due to external agents (J60-J70)

Code First
  • underlying disease, such as:
  • disorders of iron metabolism (E83.1-)
Code First
  • underlying disease, such as:
  • lung diseases due to external agents (J60-J70)
  • rheumatoid arthritis (M05.00-M06.9)
  • sarcoidosis (D86.-)
  • systemic connective tissue disorders (M30-M36)
Code First
  • underlying disease, such as:
  • progressive systemic sclerosis (M34.0)
  • rheumatoid arthritis (M05.00-M06.9)
  • systemic lupus erythematosis (M32.0-M32.9)
Code First
  • , if applicable:
  • poisoning due to drug or toxin (T51-T65 with fifth or sixth character to indicate intent), for toxic pneumonopathy
  • underlying cause of pneumonopathy, if known
Use Additional Code

code, for adverse effect, to identify drug (T36-T50 with fifth or sixth character 5), if drug-induced

Inclusion Terms

Essential brown induration of lung

Inclusion Terms
  • Capillary fibrosis of lung
  • Cirrhosis of lung (chronic) NOS
  • Fibrosis of lung (atrophic) (chronic) (confluent) (massive) (perialveolar) (peribronchial) NOS
  • Induration of lung (chronic) NOS
  • Postinflammatory pulmonary fibrosis
Inclusion Terms
  • Cryptogenic fibrosing alveolitis
  • Idiopathic fibrosing alveolitis
Inclusion Terms

Hamman-Rich syndrome

Inclusion Terms

Progressive fibrotic interstitial lung disease

Inclusion Terms
  • Interstitial pneumonia (nonspecific) (usual) due to collagen vascular disease
  • Interstitial pneumonia (nonspecific) (usual) in diseases classified elsewhere
  • Organizing pneumonia due to collagen vascular disease
  • Organizing pneumonia in diseases classified elsewhere
Inclusion Terms

Lymphoid interstitial pneumonitis

Inclusion Terms

Lymphangiomyomatosis

Inclusion Terms

Adult PLCH

Inclusion Terms
  • Endogenous lipoid pneumonia
  • Interstitial pneumonitis
  • Non-specific interstitial pneumonitis NOS
  • Organizing pneumonia NOS
Inclusion Terms

Interstitial pneumonia NOS

Code Also

, if applicable, associated condition

Child Codes (More Specific Codes for J84):

J84.0 - Alveolar and parieto-alveolar conditions J84.01 - Alveolar proteinosis J84.02 - Pulmonary alveolar microlithiasis J84.03 - Idiopathic pulmonary hemosiderosis J84.09 - Other alveolar and parieto-alveolar conditions J84.1 - Other interstitial pulmonary diseases with fibrosis J84.10 - Pulmonary fibrosis, unspecified J84.11 - Idiopathic interstitial pneumonia J84.111 - Idiopathic interstitial pneumonia, not otherwise specified J84.112 - Idiopathic pulmonary fibrosis J84.113 - Idiopathic non-specific interstitial pneumonitis J84.114 - Acute interstitial pneumonitis J84.115 - Respiratory bronchiolitis interstitial lung disease J84.116 - Cryptogenic organizing pneumonia J84.117 - Desquamative interstitial pneumonia J84.17 - Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere J84.170 - Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere J84.178 - Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere J84.2 - Lymphoid interstitial pneumonia J84.8 - Other specified interstitial pulmonary diseases J84.81 - Lymphangioleiomyomatosis J84.82 - Adult pulmonary Langerhans cell histiocytosis J84.83 - Surfactant mutations of the lung J84.84 - Other interstitial lung diseases of childhood J84.841 - Neuroendocrine cell hyperplasia of infancy J84.842 - Pulmonary interstitial glycogenosis J84.843 - Alveolar capillary dysplasia with vein misalignment J84.848 - Other interstitial lung diseases of childhood J84.89 - Other specified interstitial pulmonary diseases J84.9 - Interstitial pulmonary disease, unspecified

About ICD-10-CM Code J84 (Other interstitial pulmonary diseases)

ICD-10-CM code J84 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM J84 became effective on October 1, 2024.

This page provides detailed information about J84 - Other interstitial pulmonary diseases. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Other interstitial pulmonary diseases.