ICD-10-CM Diagnosis Code (2025)
Official Description for J84
Other interstitial pulmonary diseases
Coding Notes & Guidelines for J84
- drug-induced interstitial lung disorders (J70.2-J70.4)
- interstitial emphysema (J98.2)
acute idiopathic pulmonary hemorrhage in infants [AIPHI] (R04.81)
- pulmonary fibrosis (chronic) due to inhalation of chemicals, gases, fumes or vapors (J68.4)
- pulmonary fibrosis (chronic) following radiation (J70.1)
- lymphoid interstitial pneumonia (J84.2)
- pneumocystis pneumonia (B59)
non-specific interstitial pneumonia NOS, or due to known underlying cause (J84.89)
pneumocystis pneumonia (B59)
organizing pneumonia NOS, or due to known underlying cause (J84.89)
- exogenous lipoid pneumonia (J69.1)
- unspecified lipoid pneumonia (J69.1)
- cryptogenic organizing pneumonia (J84.116)
- idiopathic non-specific interstitial pneumonitis (J84.113)
- lipoid pneumonia, exogenous or unspecified (J69.1)
- lymphoid interstitial pneumonia (J84.2)
lung diseases due to external agents (J60-J70)
- underlying disease, such as:
- disorders of iron metabolism (E83.1-)
- underlying disease, such as:
- lung diseases due to external agents (J60-J70)
- rheumatoid arthritis (M05.00-M06.9)
- sarcoidosis (D86.-)
- systemic connective tissue disorders (M30-M36)
- underlying disease, such as:
- progressive systemic sclerosis (M34.0)
- rheumatoid arthritis (M05.00-M06.9)
- systemic lupus erythematosis (M32.0-M32.9)
- , if applicable:
- poisoning due to drug or toxin (T51-T65 with fifth or sixth character to indicate intent), for toxic pneumonopathy
- underlying cause of pneumonopathy, if known
code, for adverse effect, to identify drug (T36-T50 with fifth or sixth character 5), if drug-induced
Essential brown induration of lung
- Capillary fibrosis of lung
- Cirrhosis of lung (chronic) NOS
- Fibrosis of lung (atrophic) (chronic) (confluent) (massive) (perialveolar) (peribronchial) NOS
- Induration of lung (chronic) NOS
- Postinflammatory pulmonary fibrosis
- Cryptogenic fibrosing alveolitis
- Idiopathic fibrosing alveolitis
Hamman-Rich syndrome
Progressive fibrotic interstitial lung disease
- Interstitial pneumonia (nonspecific) (usual) due to collagen vascular disease
- Interstitial pneumonia (nonspecific) (usual) in diseases classified elsewhere
- Organizing pneumonia due to collagen vascular disease
- Organizing pneumonia in diseases classified elsewhere
Lymphoid interstitial pneumonitis
Lymphangiomyomatosis
Adult PLCH
- Endogenous lipoid pneumonia
- Interstitial pneumonitis
- Non-specific interstitial pneumonitis NOS
- Organizing pneumonia NOS
Interstitial pneumonia NOS
, if applicable, associated condition
Child Codes (More Specific Codes for J84):
About ICD-10-CM Code J84 (Other interstitial pulmonary diseases)
ICD-10-CM code J84 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM J84 became effective on October 1, 2024.
This page provides detailed information about J84 - Other interstitial pulmonary diseases. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Other interstitial pulmonary diseases.