ICD-10-CM Diagnosis Code (2025)
Official Description for J84.1
Other interstitial pulmonary diseases with fibrosis
Coding Notes & Guidelines for J84.1
- pulmonary fibrosis (chronic) due to inhalation of chemicals, gases, fumes or vapors (J68.4)
- pulmonary fibrosis (chronic) following radiation (J70.1)
- lymphoid interstitial pneumonia (J84.2)
- pneumocystis pneumonia (B59)
non-specific interstitial pneumonia NOS, or due to known underlying cause (J84.89)
pneumocystis pneumonia (B59)
organizing pneumonia NOS, or due to known underlying cause (J84.89)
- underlying disease, such as:
- lung diseases due to external agents (J60-J70)
- rheumatoid arthritis (M05.00-M06.9)
- sarcoidosis (D86.-)
- systemic connective tissue disorders (M30-M36)
- underlying disease, such as:
- progressive systemic sclerosis (M34.0)
- rheumatoid arthritis (M05.00-M06.9)
- systemic lupus erythematosis (M32.0-M32.9)
- Capillary fibrosis of lung
- Cirrhosis of lung (chronic) NOS
- Fibrosis of lung (atrophic) (chronic) (confluent) (massive) (perialveolar) (peribronchial) NOS
- Induration of lung (chronic) NOS
- Postinflammatory pulmonary fibrosis
- Cryptogenic fibrosing alveolitis
- Idiopathic fibrosing alveolitis
Hamman-Rich syndrome
Progressive fibrotic interstitial lung disease
- Interstitial pneumonia (nonspecific) (usual) due to collagen vascular disease
- Interstitial pneumonia (nonspecific) (usual) in diseases classified elsewhere
- Organizing pneumonia due to collagen vascular disease
- Organizing pneumonia in diseases classified elsewhere
Parent Code (Less Specific):
About ICD-10-CM Code J84.1 (Other interstitial pulmonary diseases with fibrosis)
ICD-10-CM code J84.1 is a billable or specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. The 2025 edition of ICD-10-CM J84.1 became effective on October 1, 2024.
This page provides detailed information about J84.1 - Other interstitial pulmonary diseases with fibrosis. It includes common terminology, coding guidelines such as "Includes," "Excludes1," and "Excludes2" notes, and information on required 7th characters. Utilizing this information correctly is essential for accurate medical coding and claims submission for conditions like Other interstitial pulmonary diseases with fibrosis.